"Butterfly Girl" loses skin with every touch
Severe congenital disease causes a seven-year resident of the UK Holly Shaw in pain every day and try to avoid the slightest injuries and bruises, writes The Daily Mail. p>
Fact that Holly suffers from epidermolysis bullosa. This is a rare inherited disorder caused by a defect of the gene, so that the body lacks a special material, which acts as "glue." Because of this, Holly skin is thin, like the wings of a butterfly, and at the slightest careless touch can be covered with blisters or even get off, as it usually happens after burns.
Even Holly esophagus does not function properly due to illness and she has to eat through a tube. Most people with the disease do not live it for more than 30 years, as the disease makes them more susceptible to certain types of cancer, and their injuries often lead to infections.
To protect the wound from infection Holly, her mother daily treats blisters. Holly takes a bath every three days, like changing clothes. All of these procedures bring her incredible pain. "When I change the bandage, she was crying and screaming," – says the mother. In addition, Holly tires to wear on the hands and feet, in order to prevent the "bonding" of her fingers during healing.
Sometimes a girl has to use a wheelchair. Her parents, walking with her, have avoided such places as parks, where other children can interfere with their daughter and cause her injury. However, Holly goes to a school where all of her friends are well aware that it is necessary to be very careful.
Surprisingly, in spite of all the troubles, the girl tries to live a full life. She roller-skates, and recently even started horse riding. "It is important that she could do it now, because it might not be able to do it, when it becomes older," – says her mother.
According to the woman, Holly was born to be completely healthy child. The only thing that was unusual – a small red mark on her finger. However, a few hours after birth, the skin on the legs Holly began to redden and blister. Analyses showed that the girl recessive dystrophic epidermolysis bullosa, caused by the presence of the defective gene, which "rewarded" her by both parents.